Iniencephaly with Anencephaly: Case Report
نویسندگان
چکیده
Iniencephaly is an extremely rare neural tube defect characterized by the triad of fixed retroflexion of the head, variable degrees of cervical lordosis and dysraphism, and an occipital bone defect involving the foramen magnum. Incidence ranges from 0.1 to 10 in 10,000. Although there have been cases of iniencephaly reported as an isolated anomaly, it very rarely occurs alone. We report here a rare case of Iniencephaly in association with anencephaly.
منابع مشابه
Congenital malformations associated with anencephaly and iniencephaly.
The necropsy reports of 294 cases of anencephaly and 50 cases of iniencephaly have been examined, and a tubulated list of associated malformations produced. Cases were divided by sex and the presence or absence of spina bifida. Forty-one per cent of the series had other malformations, and other malformations were more common in those cases with spina bifida than in those without. The most frequ...
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OBJECTIVE Iniencephaly is a rare neural tube defectwith consisting of a defect in the occipital bone,spina bifida of many vertebrae, and retroflexion of the head on the spine. In majorty of cases it is a le-\thal condition. METHODS We present the first case of iniencephalywith large bronchogenic cyst diagnosed prenatally. RESULTS At 19 week's gestation showed that fetalcardiac activity was ...
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